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A Case of Glycogen Strage Disease Type I a With Hepatocellular carcinoma
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- KOBAYASHI Noritoshi
- Department of Gastroenterological Medicine, Kanagawa Cancer Center
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- MIYAKAWA Kaoru
- Department of Gastroenterological Medicine, Kanagawa Cancer Center
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- OHKAWA Shin-ichi
- Department of Gastroenterological Medicine, Kanagawa Cancer Center
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- TAMAI Setsuo
- Department of Gastroenterological Medicine, Kanagawa Cancer Center
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- TARAO Kazuo
- Department of Gastroenterological Medicine, Kanagawa Cancer Center
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- SUGIMASA Yukio
- Department of Gastroenterological Surgery, Kanagawa Cancer Center
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- TAKEMIYA Syouji
- Department of Gastroenterological Surgery, Kanagawa Cancer Center
Bibliographic Information
- Other Title
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- 糖原病に合併した肝細胞癌の1例
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Description
33歳糖原病Ia型の男性. 3歳時に他院にて肝腫大を指摘され肝生検にて糖原病Ia型と診断された. 19歳時より多発性の肝腫瘍のため当院へ紹介され, 経過観察を行った. 腫瘍は非常に緩やかな増大傾向を示し, 一部では縮小傾向を示す部分も認められた. 32歳時に肝左葉外側区域部分切除術を施行. 組織学的に中分化が主体の肝細胞癌と診断された. その後腫瘍は急速に増大し33歳時に死亡された. 糖原病では肝細胞癌の合併は極めてまれである.
Journal
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- Kanzo
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Kanzo 43 (1), 43-49, 2002
The Japan Society of Hepatology
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Details 詳細情報について
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- CRID
- 1390282679768610432
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- NII Article ID
- 10007869535
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- NII Book ID
- AN00047770
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- ISSN
- 18813593
- 04514203
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- Text Lang
- ja
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- Data Source
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- JaLC
- Crossref
- CiNii Articles
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- Abstract License Flag
- Disallowed